WebIsolated plantar cerebriform collagenomas are a relatively rare type of connective tissue nevus. They have been suggested to be pathognomonic of Proteus syndrome. However, their presence is now considered to be a major criterion of Proteus syndrome, but the diagnosis of Proteus syndrome also requires the presence of other minor criteria. WebLate-onset Proteus syndrome with cerebriform connective tissue nevus and subsequent development of intraductal papilloma. Modlin EW, Slavotinek AM, Darling TN, Lipkowitz …

Progressive Overgrowth of the Cerebriform Connective Tissue Nevus …

WebA cerebriform connective tissue nevus is considered nearly pathognomonic for the disease but is rarely present at birth. However, linear verrucous epidermal nevi are … WebWhile this spectrum overlaps with Proteus syndrome (sporadic, mosaic, and progressive) it can be distinguished by the absence of cerebriform connective tissue nevi and a distinct natural history. Vascular malformations were found in 15/35 (43%) and epidermal nevi in 4/35 (11%) patients, lower than in Proteus syndrome. dungeon crawl stone soup 汉化

Connective tissue naevi (nevi) DermNet

WebDistinct cutaneous features, including cerebriform connective tissue nevi (CCTN), epidermal nevi, vascular malformations, and adipose abnormalities, can alert the … WebDec 31, 2015 · To overcome the diagnostic confusion, there are three general mandatory criteria with at least one of the three category signs designated as specific criteria according to First National Conference... WebCerebriform intradermal nevus (CIN) is a rare form of cutis verticis gyrata (CVG) clinically manifesting as a scalp deformity resembling surface of the brain, with … dungeon crawl ttrpg